Protein Details: Amiloride-sensitive sodium channel subunit alpha

Protein ID

ICDB_Pro_1365

Protein Name

Amiloride-sensitive sodium channel subunit alpha

Gene Name

SCNN1A; ENAC

Organism

Gallus gallus (Chicken)

Length

637 amino acids

AlphaFoldDB

AF-Q92075-F1-model_v4.pdb

Function

Sodium permeable non-voltage-sensitive ion channel inhibited by the diuretic amiloride. Mediates the electrodiffusion of the luminal sodium (and water; which follows osmotically) through the apical membrane of epithelial cells. Plays an essential role in electrolyte and blood pressure homeostasis; but also in airway surface liquid homeostasis; which is important for proper clearance of mucus.

Sequence

MGTASRGGSVKAEKMPEGEKTRQCKQETEQQQKEDEREGLIEFYGSYQDVFQFFCSNTTIHGAIRLVCSKKNKMKTAFWSVLFILTFGLMYWQFGILYREYFSYPVNLNLNLNSDRLTFPAVTLCTLNPYRYSAIRKKLDELDQITHQTLLDLYDYNMSLARSDGSAQFSHRRTSRSLLHHVQRHPLRRQKRDNLVSLPENSPSVDKNDWKIGFVLCSENNEDCFHQTYSSGVDAVREWYSFHYINILAQMPDAKDLDESDFENFIYACRFNEATCDKANYTHFHHPLYGNCYTFNDNSSSLWTSSLPGINNGLSLVVRTEQNDFIPLLSTVTGARVMVHDQNEPAFMDDGGFNVRPGIETSISMRKEMTERLGGSYSDCTEDGSDVPVQNLYSSRYTEQVCIRSCFQLNMVKRCSCAYYFYPLPDGAEYCDYTKHVAWGYCYYKLLAEFKADVLGCFHKCRKPCKMTEYQLSAGYSRWPSAVSEDWVFYMLSQQNKYNITSKRNGVAKVNIFFEEWNYKTNGESPAFTVVTLLSQLGNQWSLWFGSSVLSVMELAELILDFTVITFILAFRWFRSKQWHSSPAPPPNSHDNTAFQDEASGLDAPHRFTVEAVVTTLPSYNSLEPCGPSKDGETGLE

PDB Structures

Ligand Binding

1. DICL_CP

2. DICL_Pep

Binding Site

Disease

Location

The long isoform has been found in cochlea; colon; and cartilage. The short isoform is only found in cochlea.

DOI ID

10.1016/s0167-4781(96)00197-2

RefSeq

NP_990476.2

Feature